低热量，高营养，确保每一口都有价值
由于新陈代谢较慢，小胖患者只能消耗同龄人所能消耗的60%的千焦热量。这也只能是保持体重，如果需要减肥，那摄入的热量则应该更少。
营养起着至关重要的作用，以确保每一口都有价值。此外，小胖患者处理碳水化合物的效率较低，摄入碳水化合物后更容易发胖。
小胖患者摄入精制碳水化合物后，大脑中的奖励机制更加明显，这使他们几乎上瘾。一项为期五年的研究得出结论，低碳水化合物、适量蛋白质和优质脂肪的饮食更有益。
纤维也是饮食结构中极为重要的部分，高复合碳水化合物也主要来源于蔬菜。研究还表明，正确的饮食可以提高能量水平、学习能力、语言能力、情绪和肠道活动能力。
由于很难定期获得针对这些特殊需求的专业营养建议，父母往往被迫承担这一角色。许多父母花费无数的时间研究，然后准备饭菜。饮食的比例和份额要时刻检查和控制。
因此，当家人和朋友说来吧，多一个没什么，或你确定他吃饱了吗？或他是一个成长中的男孩，需要更多的碳水化合物时，这是非常令人沮丧的。大多数小胖的饮食是不允许有额外的东西的。
英文原文
PWS AND NUTRITION
With a slower metabolism people with PWS can only consume 60% of the kilojoules that someone else of the same age can. This is to maintain weight – less if weight loss if required.
Nutrition plays a vital role, to make sure that every mouthful counts.
Additionally, people with PWS are less effective at processing carbohydrates and put on weight much more easily when they are consumed. The reward mechanism in the brain is more pronounced with the consumption of refined carbohydrates for people with PWS, making them almost addictive.
A five-year research study concluded that a diet lower in carbohydrates, moderate in protein and increased quality fats is more beneficial. Fibre is an extremely important component of this mix also. The carbohydrates need to be complex and mostly derived from vegetables.
Research also suggests a diet rich in the right foods can improve energy levels, learning, speech, mood and gut mobility.
With regular access to expert nutritional advice for these specific needs extremely difficult to obtain, parents are often forced to undertake this role. Many parents spend countless hours researching and then preparing meals. Ratios and portions are constantly monitored and controlled.
It is therefore very disheartening when family and friends make comments like “come on, one won’t hurt” or “are you sure you’re feeding her enough” or “he’s a growing boy, he needs more carbs”. The diet of most people with PWS doesn’t allow for extras.
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公益捐款渠道
一点关怀，
或许就能为一个病人创造希望。
心有阳光，
人间便处处得见温暖。
